Crystal-storing histiocytosis kidney
WebFeb 1, 2016 · Crystal-storing histiocytosis (CSH) is a rare manifestation of monoclonal gammopathy in which histiocytes containing monoclonal proteins in their cytoplasm are found in various organs of the body ...
Crystal-storing histiocytosis kidney
Did you know?
WebThe term crystal-storing histiocytosis should be used when the crystals are noted in the histiocytes and not when the crystals are noted in the epithelial cells of the glomeruli or … WebCrystal-storing histiocytosis (CSH) is a rare complication of MM and other B-lymphocyte proliferative diseases, and can involve a wide variety of organs. The most common target is bone marrow, followed by the head and neck, with kidney ranking third [ 3 ].
WebDec 28, 2024 · Crystal-storing histiocytosis may result in a variety of clinical manifestations depending on the involved organs. Eye/orbit is 1 of the most common sites affected by CSH. [ 12 ] Involvement of the cornea (“crystalline keratopathy”) is well described, and CSH has been also reported to involve the conjunctiva, the orbital fat, and extra ... WebJan 3, 2009 · Crystal storing histiocytosis (CSH) is a very rare disorder characterized by accumulation of monoclonal immunoglobulin light chains within histiocytes. Herein, we present a case of CSH associated with multiple myeloma (MM). ... Siegel D et al (2006) Dysproteinemia-related nephropathy associated with crystal-storing histiocytosis. Kidney …
WebMar 30, 2024 · Combined proximal tubulopathy, crystal-storing histiocytosis, and cast nephropathy in a patient with light chain multiple myeloma. Wu CK, Yang AH, Lai HC, et al. BMC Nephrol. 2024;18:170. Acquired Fanconi syndrome is an indolent disorder in the absence of overt multiple myeloma. Ma CX, Lacy MQ, Rompala JF, et al. Blood. … WebOct 20, 2024 · Crystal-storing histiocytosis (CSH) is a unique entity presenting as sheets of histiocytes with accumulation of crystalline matter within the cytoplasm. It can present as either a localized or generalized disease and has a variable outcome depending on the underlying CSH etiology [ 1 ].
WebJan 1, 2002 · Although crystal-storing histiocytosis has been reported in the bone marrow and several organs in association with plasmacytic tumors, there is only one report in …
WebMay 1, 2024 · Crystal-storing histiocytosis is an exceedingly rare paraprotein-associated disease that is typically systemic and rarely involves the kidney. 40 By light microscopic evaluation a chronic tubulointerstitial nephritis is present with abundant interstitial histiocytes. Within the histiocytes, crystals are deposited that show similar morphologies ... biopath vendinWebMar 20, 2012 · Crystal-storing histiocytosis (CSH), a rare condition in which crystalline material accumulates in the cytoplasm of histiocytes, is typically associated with disorders that express monoclonal immunoglobulins, such as multiple myeloma (MM), lymphoplasmacytic lymphoma (LPL), and monoclonal gammopathy of undetermined … daine raymour and flaniganWebCrystal-bearing or crystal-storing histiocytosis (CSH) is a rare mor-phologic manifestation of monoclonal gammopathy in which monoclonal crystals, usually belonging to kappa subtype and having various geometric shapes, collect within histiocytes that, via systemic circulation, end up in various organs [2-9]. In the kidney, such histio- dainely belt reviewsWebNational Center for Biotechnology Information biopath yerresWebAug 30, 2024 · Crystal-storing histiocytosis is a rare disorder that is morphologically characterized by the accumulation of monoclonal immunoglobulin crystals, predominantly of a kappa light chain type, within lysosomes of macrophages. biopaw pickeringWebAug 1, 2024 · Crystal-storing histiocytosis (CSH) is an extremely rare disorder in which immunoglobulins accumulate abnormally in the cytoplasm of histiocytes, appearing as … daine round ottomanWebApr 12, 2024 · Die Bezeichnung monoklonale Gammopathie renaler Signifikanz (MGRS) wurde vor einigen Jahren als neuer Oberbegriff eingeführt für Nierenerkrankungen durch Produktion von monoklonalen Immunglobulinen eines B‑Zell-Klons, der nicht die Kriterien für … dain conway tax services